Acidúria Isovalérica[vc_row row_height_percent=”0″ override_padding=”yes” h_padding=”2″ top_padding=”5″ bottom_padding=”5″ back_color=”color-wayh” back_image=”88431″ overlay_color=”color-wayh” overlay_alpha=”50″ gutter_size=”3″ column_width_percent=”100″ shift_y=”0″ z_index=”0″ shape_dividers=””][vc_column column_width_use_pixel=”yes” position_vertical=”middle” align_horizontal=”align_center” gutter_size=”3″ style=”light” overlay_alpha=”50″ shift_x=”0″ shift_y=”0″ shift_y_down=”0″ z_index=”0″ medium_width=”0″ mobile_width=”0″ width=”1/1″ column_width_pixel=”900″][vc_custom_heading heading_semantic=”h6″ text_size=”fontsize-160000″ text_transform=”uppercase” text_space=”fontspace-210350″ text_color=”color-xsdn” css_animation=”alpha-anim”]Área terapêutica[/vc_custom_heading][vc_custom_heading heading_semantic=”h1″ text_size=”h1″ text_color=”color-xsdn” sub_reduced=”yes” css_animation=”alpha-anim” animation_delay=”600″ el_class=”margin-0″]Acidúria Isovalérica[/vc_custom_heading][/vc_column][/vc_row][vc_row][vc_column width=”1/1″][uncode_block id=”88285″][/vc_column][/vc_row][vc_row][vc_column width=”1/1″][uncode_block id=”88338″][/vc_column][/vc_row][vc_row row_height_percent=”0″ override_padding=”yes” h_padding=”2″ top_padding=”5″ bottom_padding=”5″ back_color=”color-lxmt” overlay_alpha=”50″ gutter_size=”3″ column_width_percent=”100″ shift_y=”0″ z_index=”0″][vc_column width=”1/1″][vc_row_inner limit_content=””][vc_column_inner width=”1/2″][vc_custom_heading heading_semantic=”h3″]A Acidúria Isovalérica é uma doença hereditária do metabolismo da leucina, que resulta do défice de uma enzima, o que provoca acumulação de ácido isovalérico.[/vc_custom_heading][/vc_column_inner][vc_column_inner column_width_percent=”100″ gutter_size=”3″ overlay_alpha=”50″ shift_x=”0″ shift_y=”0″ shift_y_down=”0″ z_index=”0″ medium_visibility=”yes” medium_width=”0″ mobile_visibility=”yes” mobile_width=”0″ width=”1/2″][/vc_column_inner][/vc_row_inner][vc_row_inner row_inner_height_percent=”0″ overlay_alpha=”50″ gutter_size=”4″ shift_y=”0″ z_index=”0″ limit_content=””][vc_column_inner width=”1/2″][vc_column_text]O tratamento consiste numa dieta restrita em proteína e leucina e suplementada em carnitina e glicina, concomitante com o tratamento farmacológico.[/vc_column_text][/vc_column_inner][vc_column_inner column_width_percent=”100″ gutter_size=”3″ overlay_alpha=”50″ shift_x=”0″ shift_y=”0″ shift_y_down=”0″ z_index=”0″ medium_visibility=”yes” medium_width=”0″ mobile_visibility=”yes” mobile_width=”0″ width=”1/2″][vc_column_text]Pode ser necessário introduzir na dieta uma fórmula de aminoácidos isenta de leucina, que pode ser líquida ou em pó, adequada às várias fases do crescimento.[/vc_column_text][vc_column_text text_lead=”small”]1. Sociedade Portuguesa de Pediatria. Consenso para o tratamento nutricional das acidúrias isovalérica, propiónica e metilmalónica. Acta Pediátrica Portuguesa. 2008. 2. Gick Jane. Acidúrias Orgânicas – Guia para doentes, pais e famílias. EIMD[/vc_column_text][/vc_column_inner][/vc_row_inner][/vc_column][/vc_row][vc_row row_height_percent=”0″ override_padding=”yes” h_padding=”2″ top_padding=”5″ bottom_padding=”5″ overlay_alpha=”50″ gutter_size=”2″ column_width_percent=”100″ shift_y=”0″ z_index=”0″][vc_column column_width_percent=”100″ gutter_size=”4″ overlay_alpha=”50″ shift_x=”0″ shift_y=”0″ shift_y_down=”0″ z_index=”0″ medium_width=”0″ mobile_width=”0″ width=”1/1″][vc_custom_heading]Produtos[/vc_custom_heading][uncode_index el_id=”index-609212479″ isotope_mode=”fitRows” loop=”size:1|order_by:date|post_type:portfolio|taxonomy_count:10″ gutter_size=”3″ post_items=”media|featured|onpost|poster,date,title,text|excerpt|90,category|bordered|topright|hide-icon” portfolio_items=”media|featured|onpost|original,title,text|excerpt” screen_lg=”1000″ screen_md=”600″ screen_sm=”480″ single_width=”3″ images_size=”one-one” single_overlay_color=”accent” single_overlay_opacity=”50″ single_h_align=”center” single_padding=”1″ single_title_semantic=”p” single_title_dimension=”fontsize-138891″ single_border=”yes” single_icon=”fa fa-plus2″][/vc_column][/vc_row]